Abstract:
Amyloidosis is caused by abnormal protein deposition in various tissues, including the lungs. Pulmonary manifestations of amyloidosis may be categorized by areas of involvement, such as parenchymal, large airway and pleural involvement. We describe four distinct manifestations of amyloidosis involving the lung and review their clinical, radiological and pathological features and summarize the evidence for treatment in each of these presentations. We describe alveolar-septal amyloidosis, cystic amyloid lung disease, endobronchial amyloidosis and pleural amyloidosis.
摘要:
淀粉样变是由各种组织中的异常蛋白质沉积引起的,包括肺.淀粉样变性的肺部表现可按受累区域分类,比如实质,大气道和胸膜受累。我们描述了淀粉样变性累及肺部的四种不同表现,并回顾了它们的临床,放射学和病理学特征,并总结这些表现中的治疗证据。我们描述了肺泡间隔淀粉样变,囊性淀粉样肺病,支气管内淀粉样变性和胸膜淀粉样变性。