关键词: Case report Computed tomography angiography Echocardiogram Pulmonary arteritis Takayasu arteritis

来  源:   DOI:10.1186/s43044-023-00416-8   PDF(Pubmed)

Abstract:
BACKGROUND: Takayasu arteritis (TAK) is a chronic inflammatory arteritis. It most often affects non-specific large vessel progressively, such as the aorta and its branches. The diagnosis in TAK is typically delayed. Isolated pulmonary artery involvement in Takayasu arteritis is uncommon. Owing to its rarity, the diagnosis is challenging and requires an integrated approach comprising clinical and imaging findings. In order to facilitate early diagnosis of TAK for clinicians, wider use of non-invasive imaging is impacting this.
METHODS: In this report, we present the imaging characteristics of a rare isolated pulmonary artery involvement in Takayasu arteritis. Pulmonary computed tomography angiography revealed only limited thick walls of both proximal pulmonary artery and stenosis of pulmonary artery lumen, and the other large blood vessels were not involved. The patient undergone pulmonary endarterectomy and pulmonary angioplasty. Then, approximately one month afterward, she passed away due to heart failure.
CONCLUSIONS: Imaging examination is the main basis for diagnosing this disease. This impression might improve disease awareness among doctors and progress in diagnosis.
摘要:
背景:大动脉炎(TAK)是一种慢性炎症性动脉炎。它通常会逐渐影响非特异性大血管,如主动脉及其分支。TAK的诊断通常会延迟。孤立性肺动脉累及大动脉炎并不常见。由于它的稀有性,诊断具有挑战性,需要采用包括临床和影像学检查结果的综合方法.为了方便临床医生早期诊断TAK,非侵入性成像的广泛应用正在影响这一点。
方法:在本报告中,我们介绍了罕见的孤立性大动脉炎肺动脉受累的影像学特征.肺计算机断层扫描血管造影仅显示近端肺动脉壁有限,肺动脉管腔狭窄,和其他大血管没有参与。患者接受了肺内膜切除术和肺血管成形术。然后,大约一个月后,她因心力衰竭去世了。
结论:影像学检查是诊断本病的主要依据。这种印象可能会提高医生对疾病的认识并提高诊断水平。
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