关键词: case report hyperdense vasculature secondary polycythemia tetralogy of fallot(TOF)

来  源:   DOI:10.1097/MS9.0000000000001234   PDF(Pubmed)

Abstract:
UNASSIGNED: Tetralogy of Fallot is a cyanotic congenital heart disease which if untreated leads to death by adulthood. In rare cases who survive this can lead to secondary polycythemia due to chronic hypoxia who can present with multiple indistinct symptoms leading to diagnostic dilemma.
UNASSIGNED: The authors present a rare case of secondary polycythemia diagnosed in early fifties with the unique non-contrast computerized tomography head findings who presented with a spectrum of long standing symptoms and a history of neurological manifestations.
UNASSIGNED: Patients diagnosed with polycythemia in adulthood can have a background of an untreated congenital heart disease, which can be complemented further by appropriate radiological investigations in a resource poor setting.
UNASSIGNED: Polycythemia secondary to an untreated congenital heart disease in the age beyond 50 is a rare occurrence. The presentation of these patients might present clinicians with a diagnostic challenge which can be mitigated with an appropriate knowledge of the peculiar non-contrast computerized tomography head findings.
摘要:
法洛氏四联症是一种紫红色先天性心脏病,如果不及时治疗会导致成年后死亡。在极少数情况下,如果存活下来,这可能会由于慢性缺氧而导致继发性红细胞增多症,并可能出现多种不明显的症状,从而导致诊断困境。
作者介绍了一例罕见的继发性红细胞增多症病例,在50年代早期被诊断为具有独特的非对比计算机断层扫描头颅表现,表现出一系列长期症状和神经系统表现史。
在成年期被诊断为红细胞增多症的患者可能具有未经治疗的先天性心脏病的背景,可以通过在资源贫乏的环境中进行适当的放射学调查来进一步补充。
年龄超过50岁的先天性心脏病继发红细胞增多症是罕见的。这些患者的表现可能会给临床医生带来诊断挑战,可以通过适当了解特殊的非对比计算机断层扫描头部发现来缓解这种挑战。
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