关键词: Kartagener syndrome infertility lung infection special care dentistry

Mesh : Humans Male Adult Kartagener Syndrome / therapy complications Dental Care for Chronically Ill

来  源:   DOI:10.1111/scd.12917

Abstract:
BACKGROUND: Kartagener syndrome (KS) is recognized as an inherited, autosomal recessive disorder characterized by a combination of chronic sinusitis, bronchiectasis, and situs inversus. It affects one in 12,500-50,000 live births worldwide.
OBJECTIVE: This paper aims to discuss the dental management of patients diagnosed with KS.
METHODS: A 31-year-old male with KS manifests by impaired cilia motility which increases the risk of a frequent lung infection. The dental examination revealed that the patient required comprehensive oral hygiene care which included patient education and nonsurgical periodontal therapy under local anesthesia.
CONCLUSIONS: Dental care providers should ask affected patients with KS about their signs and symptoms of cardiac and pulmonary disease and seek consultation with their attending physician regarding these health concerns before the initiation of general anesthesia and perhaps conscious sedation administration. Patients with KS with emerging cardiac and/or respiratory impairment should be referred promptly for medical assessment.
摘要:
背景:Kartagener综合征(KS)被认为是一种遗传性,以慢性鼻窦炎为特征的常染色体隐性遗传疾病,支气管扩张,和Situs倒置。它影响到全世界每12,500-50,000个活产中就有一个。
目的:本文旨在讨论诊断为KS的患者的牙科管理。
方法:一名31岁男性KS患者表现为纤毛运动受损,这增加了频繁肺部感染的风险。牙科检查显示,患者需要全面的口腔卫生护理,包括患者教育和局部麻醉下的非手术牙周治疗。
结论:牙科护理提供者应询问受影响的KS患者的心脏和肺部疾病的体征和症状,并在开始全身麻醉和清醒镇静之前就这些健康问题咨询主治医师。出现心脏和/或呼吸损害的KS患者应及时转诊以进行医学评估。
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