关键词: cardiac magnetic resonance imaging computed tomography echocardiogram multimodal imaging pericardial synovial sarcoma

来  源:   DOI:10.3389/fonc.2023.1181778   PDF(Pubmed)

Abstract:
UNASSIGNED: Primary pericardial synovial sarcoma is an extremely rare malignant tumor, and affected patients have a poor prognosis. Only a few cases have been reported in the literature.
UNASSIGNED: A 34-year-old man was admitted to our hospital with chest tightness and a cough. An echocardiogram revealed a heterogeneous mass with a large pericardial effusion. Further computed tomography (CT) of the chest and cardiac magnetic resonance imaging (CMRI) demonstrated an irregular pericardial mass abutting the left atrium and left ventricle and invading the mediastinal structures. Pathology results showed that the tumor was a monophasic synovial sarcoma. The patient underwent chemotherapy and survived for 17 months.
UNASSIGNED: Many cardiac tumors are clinically asymptomatic or nonspecific, and they are frequently detected or diagnosed at an advanced stage of the disease. Multimodal cardiac imaging facilitates the detection and assessment of cardiac tumors. In particular, CMRI is considered as a superior imaging tool, because it provides high tissue contrast and can detect invasion of the myocardium. We describe the clinical details and multimodal imaging features of a rare primary pericardial synovial sarcoma, hoping to provide guidance for the diagnosis of similar cases in the future.
摘要:
原发性心包滑膜肉瘤是一种极为罕见的恶性肿瘤,和受影响的患者预后差。文献中仅报道了少数病例。
一名34岁男子因胸闷和咳嗽入院。超声心动图显示有大量的心包积液。胸部和心脏磁共振成像(CMRI)的进一步计算机断层扫描(CT)显示出不规则的心包肿块邻接左心房和左心室并侵入纵隔结构。病理结果显示肿瘤为单相滑膜肉瘤。患者接受化疗,存活17个月。
许多心脏肿瘤在临床上无症状或非特异性,他们经常在疾病的晚期被发现或诊断出来。多模式心脏成像有助于心脏肿瘤的检测和评估。特别是,CMRI被认为是一种卓越的成像工具,因为它提供了很高的组织对比度,可以检测心肌的侵入。我们描述了罕见的原发性心包滑膜肉瘤的临床细节和多模态成像特征,希望为今后类似病例的诊断提供指导。
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