Abstract：
We aim to share the diagnostic methods and relevant findings of a rare case involving a 1-year-old girl with a variation of Shone syndrome, presenting with the coexistence of a single coronary artery and a fistula between the coronary artery and the right pulmonary artery. The patient had previously undergone aortic arch reconstruction surgery and during the preoperative evaluation, cardiac computed tomography angiography (CCTA) revealed the additional presence of a single coronary artery originating from the right, which fistulized into the right pulmonary artery distally. This finding was further confirmed by conventional angiography. This case report highlights the importance of CCTA in identifying and directing the treatment of additional anomalies that may accompany rare congenital abnormalities.
摘要：
我们的目的是分享一个罕见病例的诊断方法和相关发现，该病例涉及一名1岁女孩患有Shone综合征的变异，表现为单个冠状动脉和冠状动脉与右肺动脉之间的瘘共存。该患者先前曾接受过主动脉弓重建手术，在术前评估期间，心脏计算机断层扫描血管造影（CCTA）显示，来自右侧的单个冠状动脉的额外存在，造瘘进入远端右肺动脉。常规血管造影进一步证实了这一发现。此病例报告强调了CCTA在识别和指导可能伴随罕见先天性异常的其他异常的治疗中的重要性。
