Abstract:
We present the clinical course and echocardiographic and genetic findings of two fetuses with an unusual vascular ring, created by a left aortic arch with a right arterial duct and an aberrant right subclavian artery. One fetus was diagnosed with 22q11.2 microdeletion and the other became symptomatic in infancy. It is important to consider the position of the arterial ductal ligament in patients who present with tracheoesophageal compressive symptoms in the presence of a left aortic arch. These cases also highlight that a vascular ring formed from a left arch may have similar associations to a vascular ring formed by a right aortic arch.
摘要:
我们介绍了两个具有异常血管环的胎儿的临床过程以及超声心动图和遗传发现,由带有右动脉导管和异常的右锁骨下动脉的左主动脉弓产生。一个胎儿被诊断为22q11.2微缺失,另一个在婴儿期出现症状。在存在左主动脉弓的情况下存在气管食管压迫症状的患者中,重要的是要考虑动脉导管韧带的位置。这些病例还突出表明,由左主动脉弓形成的血管环可能与由右主动脉弓形成的血管环具有相似的关联。