PDF(Pubmed)
Abstract：
UNASSIGNED: Rhabdoid meningiomas (RMs) are a rare type of malignant meningioma. Here, we report a case of intracranial RM presenting with visual disturbance and prominent hyperintensity in the optic nerve (ON).
UNASSIGNED: A 20-year-old female presented with a 1-year history of headache. At presentation, her visual acuity (VA) was 20/50 on the right side and 20/40 on the left, with an intraocular pressure of 17 mmHg on both sides. Cerebral magnetic resonance imaging revealed a broad-based tumor in the right frontal convexity. It measured 82 mm × 65 mm × 70 mm in diameter, accompanied by cystic components, and was inhomogeneously enhanced. The intraorbital ONs demonstrated prominent intramedullary hyperintensity on the constructive interference steady-state sequence. Gross total tumor resection was performed and the pathology was consistent with RM. Immediately after surgery, her VA and IOP were 20/17 and 10 mmHg, respectively, with a remarkable resolution of the intramedullary hyperintensity.
UNASSIGNED: Prominent hyperintensity in the ON identified in patients with chronic intracranial hypertension may be an indicator of visual disturbance. It can rapidly resolve after resolution of intracranial hypertension with functional recovery.
UNASSIGNED: A 20-year-old female presented with a 1-year history of headache. At presentation, her visual acuity (VA) was 20/50 on the right side and 20/40 on the left, with an intraocular pressure of 17 mmHg on both sides. Cerebral magnetic resonance imaging revealed a broad-based tumor in the right frontal convexity. It measured 82 mm × 65 mm × 70 mm in diameter, accompanied by cystic components, and was inhomogeneously enhanced. The intraorbital ONs demonstrated prominent intramedullary hyperintensity on the constructive interference steady-state sequence. Gross total tumor resection was performed and the pathology was consistent with RM. Immediately after surgery, her VA and IOP were 20/17 and 10 mmHg, respectively, with a remarkable resolution of the intramedullary hyperintensity.
UNASSIGNED: Prominent hyperintensity in the ON identified in patients with chronic intracranial hypertension may be an indicator of visual disturbance. It can rapidly resolve after resolution of intracranial hypertension with functional recovery.
摘要：
■横纹肌样脑膜瘤（RM）是一种罕见的恶性脑膜瘤。这里,我们报告了一例颅内RM，表现为视觉障碍和视神经（ON）明显的高强度。
■一名20岁女性，有1年的头痛史。在介绍时,她的视力（VA）右侧是20/50，左侧是20/40，两侧的眼压为17mmHg。脑磁共振成像显示右额叶凸面有广泛的肿瘤。直径82mm×65mm×70mm,伴随着囊性成分，并且不均匀地增强。眶内ON在建设性干扰稳态序列上表现出明显的髓内高强度。进行大体肿瘤全切除，病理符合RM。手术后立即，她的VA和IOP分别为20/17和10mmHg，分别,具有显着的髓内高强度分辨率。
■在患有慢性颅内高压的患者中，在ON中发现的明显的高强度可能是视觉障碍的指标。颅内高压消退后可迅速消退，功能恢复。
■一名20岁女性，有1年的头痛史。在介绍时,她的视力（VA）右侧是20/50，左侧是20/40，两侧的眼压为17mmHg。脑磁共振成像显示右额叶凸面有广泛的肿瘤。直径82mm×65mm×70mm,伴随着囊性成分，并且不均匀地增强。眶内ON在建设性干扰稳态序列上表现出明显的髓内高强度。进行大体肿瘤全切除，病理符合RM。手术后立即，她的VA和IOP分别为20/17和10mmHg，分别,具有显着的髓内高强度分辨率。
■在患有慢性颅内高压的患者中，在ON中发现的明显的高强度可能是视觉障碍的指标。颅内高压消退后可迅速消退，功能恢复。
