关键词: Glossopharyngeal nerve Neck mass Rare Schwannoma

来  源:   DOI:10.1016/j.ijscr.2023.108629   PDF(Pubmed)

Abstract:
UNASSIGNED: Schwannomas are tumors of the nerve sheath that consist of Schwann cells that are often described as slow-growing. Glossopharyngeal schwannomas are rare tumors present in the region of the posterior fossa, with limited case reports present in literature. While patients may present asymptomatically, some present with vestibulocochlear symptoms or lower cranial nerve dysfunction.
METHODS: We report an extremely rare case of a left para-pharyngeal carotid space glossopharyngeal schwannoma in a 26-year-old female. The presentation was a 3-month left sided neck swelling and a hoarse voice. Radiological investigations were completed (neck ultrasound; CT; MRI scans). Investigations revealed a solid lesion measuring about 29 × 10 mm. The final decision was to excise the mass under microsurgery.
UNASSIGNED: CN 9-11 schwannomas are often called jugular foramen schwannomas. Intraoperatively, these get differentiated as glossopharyngeal schwannomas. Diagnosis involves a physical examination, a detailed history, audiological assessments, and radiological investigations. While MRI scans are known as the most effective pre-operative diagnostic test, cases are in majority discovered intra-operatively. Surgical excision is the recommended approach. Post-operative recurrence is rare. Pre-operative diagnosis is often difficult due to the rarity and similarly presenting differential diagnoses.
CONCLUSIONS: Schwannomas of the glossopharyngeal nerve are extremely rare tumors that may present with lower cranial nerve or vestibulocochlear deficits. Magnetic resonance imaging is a useful tool in diagnosing this unordinary tumor. This case report intends to provide further data regarding the clinical presentation, the patient population, and the diagnostic and surgical approach in dealing with this incredibly rare tumor.
摘要:
神经鞘瘤是神经鞘的肿瘤,由通常被描述为缓慢生长的雪旺氏细胞组成。舌咽神经鞘瘤是存在于后颅窝区域的罕见肿瘤,文献中的病例报告有限。虽然患者可能无症状出现,一些存在前庭耳蜗症状或下颅神经功能障碍。
方法:我们报告了一例极为罕见的26岁女性左咽旁颈动脉间隙舌咽神经鞘瘤。表现为3个月的左侧颈部肿胀和嘶哑的声音。完成放射学检查(颈部超声;CT;MRI扫描)。调查显示有一个约29×10mm的实体病变。最终的决定是在显微外科手术下切除肿块。
CN9-11神经鞘瘤通常被称为颈静脉孔神经鞘瘤。术中,这些被分化为舌咽神经鞘瘤。诊断包括体检,详细的历史,听力学评估,和放射学调查。虽然MRI扫描被认为是最有效的术前诊断测试,大多数病例在术中发现。手术切除是推荐的方法。术后复发罕见。由于稀有性和类似的鉴别诊断,术前诊断通常很困难。
结论:舌咽神经神经鞘瘤是极其罕见的肿瘤,可能存在下颅神经或前庭耳蜗缺陷。磁共振成像是诊断这种异常肿瘤的有用工具。本病例报告旨在提供有关临床表现的进一步数据,患者群体,以及治疗这种罕见肿瘤的诊断和手术方法。
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