PDF(Pubmed)
Abstract：
UNASSIGNED: The aim of this case report is to describe the dentofacial manifestations of achondroplasia and highlight concerns associated with dental management of pediatric patients with achondroplasia.
UNASSIGNED: Achondroplasia is the most common form of skeletal dysplasia (dwarfism) with clinical manifestations including disproportionate limb shortening and stunted stature. The craniofacial characteristics of achondroplasia are relative macrocephaly, depression of the nasal bridge, and maxillary hypoplasia. Special precautions are necessary during dental management of pediatric patients with achondroplasia due to a large head size, implanted shunts, airway obstruction, and difficulty in head control.
UNASSIGNED: A 6 years and 7 months male, the patient was diagnosed with achondroplasia, currently receiving vitamin D, no known drug allergy, and a mixed dentition stage with multiple caries, mouth breather, and a high risk of further caries based on a caries risk assessment due to poor oral hygiene. As the patient was uncooperative and required extensive dental care, dental rehabilitation was conducted under general anesthesia using oral intubation due to nasal obstruction. Future examinations were planned for every 3 months.
UNASSIGNED: The current case demonstrated that the characteristics of achondroplasia might cause respiratory, neurological, skeletal, orthodontic, and psychological difficulties. Pediatric dentists who treat these patients must be able to detect these characteristics and difficulties, as dental treatment is limited by practical issues associated with this condition.
UNASSIGNED: The characteristic features of achondroplasia are attributed to skeletal, respiratory, neurologic, orthodontic, and psychosocial issues. The dentist should be aware of the features of achondroplasia, which can potentially restrict dental management.
UNASSIGNED: Almutiry A, Alotaibi F, Almutiry B, et al. Craniofacial and Dental Manifestations in Pediatric Patients with Achondroplasia: A Case Report and Clinical View. Int J Clin Pediatr Dent 2023;16(2):409-415.
UNASSIGNED: Achondroplasia is the most common form of skeletal dysplasia (dwarfism) with clinical manifestations including disproportionate limb shortening and stunted stature. The craniofacial characteristics of achondroplasia are relative macrocephaly, depression of the nasal bridge, and maxillary hypoplasia. Special precautions are necessary during dental management of pediatric patients with achondroplasia due to a large head size, implanted shunts, airway obstruction, and difficulty in head control.
UNASSIGNED: A 6 years and 7 months male, the patient was diagnosed with achondroplasia, currently receiving vitamin D, no known drug allergy, and a mixed dentition stage with multiple caries, mouth breather, and a high risk of further caries based on a caries risk assessment due to poor oral hygiene. As the patient was uncooperative and required extensive dental care, dental rehabilitation was conducted under general anesthesia using oral intubation due to nasal obstruction. Future examinations were planned for every 3 months.
UNASSIGNED: The current case demonstrated that the characteristics of achondroplasia might cause respiratory, neurological, skeletal, orthodontic, and psychological difficulties. Pediatric dentists who treat these patients must be able to detect these characteristics and difficulties, as dental treatment is limited by practical issues associated with this condition.
UNASSIGNED: The characteristic features of achondroplasia are attributed to skeletal, respiratory, neurologic, orthodontic, and psychosocial issues. The dentist should be aware of the features of achondroplasia, which can potentially restrict dental management.
UNASSIGNED: Almutiry A, Alotaibi F, Almutiry B, et al. Craniofacial and Dental Manifestations in Pediatric Patients with Achondroplasia: A Case Report and Clinical View. Int J Clin Pediatr Dent 2023;16(2):409-415.
摘要：
■本病例报告的目的是描述软骨发育不全的牙面部表现，并强调与儿童软骨发育不全患者的牙科治疗相关的问题。
■软骨发育不全是骨骼发育不良（侏儒症）的最常见形式，其临床表现包括不成比例的肢体缩短和发育不良。软骨发育不全的颅面特征是相对大头畸形，鼻梁凹陷，上颌骨发育不全.特殊的预防措施是必要的在牙科治疗儿童患者软骨发育不全，由于一个大的头，植入分流器,气道阻塞,头部控制困难。
■6岁零7个月的男性，病人被诊断患有软骨发育不全,目前正在接受维生素D，没有已知的药物过敏，和多个龋齿的混合牙列阶段，嘴巴呼吸，根据龋齿风险评估，由于口腔卫生差，进一步龋齿的风险很高。由于病人不合作，需要广泛的牙科护理，由于鼻塞，在全身麻醉下使用口腔插管进行牙科康复。未来的检查计划为每3个月。
■当前病例表明软骨发育不全的特征可能会引起呼吸，神经学,骨骼，正畸,和心理上的困难。治疗这些患者的儿科牙医必须能够发现这些特征和困难，因为牙科治疗受到与这种情况相关的实际问题的限制。
■软骨发育不全的特征归因于骨骼，呼吸,神经学，正畸,和心理社会问题。牙医应该意识到软骨发育不全的特征，这可能会限制牙科管理。
■AlmutiryA，AlotaibiF,AlmutiryB,etal.儿童软骨发育不全患者的颅面和牙齿表现：病例报告和临床观点。IntJClinPediatrDent2023；16(2)：409-415。
■软骨发育不全是骨骼发育不良（侏儒症）的最常见形式，其临床表现包括不成比例的肢体缩短和发育不良。软骨发育不全的颅面特征是相对大头畸形，鼻梁凹陷，上颌骨发育不全.特殊的预防措施是必要的在牙科治疗儿童患者软骨发育不全，由于一个大的头，植入分流器,气道阻塞,头部控制困难。
■6岁零7个月的男性，病人被诊断患有软骨发育不全,目前正在接受维生素D，没有已知的药物过敏，和多个龋齿的混合牙列阶段，嘴巴呼吸，根据龋齿风险评估，由于口腔卫生差，进一步龋齿的风险很高。由于病人不合作，需要广泛的牙科护理，由于鼻塞，在全身麻醉下使用口腔插管进行牙科康复。未来的检查计划为每3个月。
■当前病例表明软骨发育不全的特征可能会引起呼吸，神经学,骨骼，正畸,和心理上的困难。治疗这些患者的儿科牙医必须能够发现这些特征和困难，因为牙科治疗受到与这种情况相关的实际问题的限制。
■软骨发育不全的特征归因于骨骼，呼吸,神经学，正畸,和心理社会问题。牙医应该意识到软骨发育不全的特征，这可能会限制牙科管理。
■AlmutiryA，AlotaibiF,AlmutiryB,etal.儿童软骨发育不全患者的颅面和牙齿表现：病例报告和临床观点。IntJClinPediatrDent2023；16(2)：409-415。
