PDF(Pubmed)
Abstract：
Peripheral nerve hyperexcitability is a rare disorder characterized by spontaneous motor unit activity. Although peripheral nerve hyperexcitability is seen in multiple immune-mediated neurological conditions, an association with dermatomyositis has rarely been reported. We present a 65-year-old woman with serological and muscle biopsy features of dermatomyositis who also developed marked muscle hypertrophy, stiffness, and delayed relaxation along with electrodiagnostic features of peripheral nerve hyperexcitability such as that seen in Isaacs syndrome.
摘要：
周围神经兴奋过度是一种罕见的疾病，其特征是自发的运动单位活动。尽管周围神经兴奋过度见于多种免疫介导的神经系统疾病，与皮肌炎相关的报道很少。我们介绍了一名65岁的女性，患有皮肌炎的血清学和肌肉活检特征，她也出现了明显的肌肉肥大，刚度,和延迟松弛以及周围神经兴奋过度的电诊断特征，例如在Isaacs综合征中看到的。
