PDF(Pubmed)
Abstract：
Epithelioid emangioendothelioma (EHE) is a rare tumor originating from vascular endothelial cells, which belongs to malignant vascular tumors with low to moderate differentiation and potential metastatic ability and its incidence rate is less than one in a million. We herein report a rare case of EHE of pulmonary origin and a review of the literature concerning the clinical and pathological features of this disease. The patient underwent left upper lobectomy to completely extirpate the lesion by video-assisted thoracic surgery. Our findings suggest the difficulty of making a diagnosis before surgery and that more cases need to be reported in order to facilitate the preoperative diagnosis of such a rare tumor.
摘要：
上皮样血管内皮瘤(EHE)是一种起源于血管内皮细胞的罕见肿瘤，属于低分化和潜在转移能力强的恶性血管肿瘤，发病率不到百万分之一。我们在此报告了一例罕见的肺部EHE病例，并回顾了有关该疾病的临床和病理特征的文献。患者接受了左上叶切除术，以通过电视辅助胸腔镜手术完全切除病变。我们的发现表明，在手术前进行诊断很困难，需要报告更多病例，以促进这种罕见肿瘤的术前诊断。
