PDF(Pubmed)
Abstract：
Desmoplastic fibroma is a rare primary benign bone tumour that typically affects the long bones, mandible, and pelvis. It has a similar local aggressiveness to soft tissue fibromatosis. It rarely involves the small bones of the hand. We describe an extremely rare case of desmoplastic fibroma of the proximal phalanx of the hand in a patient who presented with an aggressively enlarging but painless mass on the left ring finger. Radiological features suggested malignancy; however, an initial biopsy revealed fibrotic tissue. Trans-metacarpal amputation of the ring and little fingers and soft tissue reconstruction were performed using a local ulnar-based flap of the little finger. The final histopathological evaluation revealed desmoplastic fibroma. Aggressively growing masses in the hand should be treated according to a sarcoma management protocol, and desmoplastic fibroma should be included in the differential diagnosis.
摘要：
纤维增生性纤维瘤是一种罕见的原发性良性骨肿瘤，通常会影响长骨，下颌骨,还有骨盆.它具有与软组织纤维瘤病相似的局部侵袭性。它很少涉及手的小骨头。我们描述了一种极为罕见的病例，该患者的手部近端指骨的纤维增生性纤维瘤，该患者的左无名指上有明显扩大但无痛的肿块。放射学特征提示恶性肿瘤；然而，最初的活检显示纤维化组织。使用小指的局部尺骨皮瓣进行无名指和小指的掌骨截肢和软组织重建。最终的组织病理学评估显示纤维增生性纤维瘤。手部剧烈增长的肿块应根据肉瘤管理方案进行治疗，鉴别诊断应包括纤维增生性纤维瘤。
