PDF(Pubmed)
Abstract：
Alveolar soft part sarcoma (ASPS) is a rare type of soft tissue sarcoma that typically affects adolescents and young adults, though it can occur at any age. We report a case of ASPS of the tongue, which is extremely rare at this location. The patient presented with a polypoidal lesion on the tongue, a biopsy of which showed granular and alveolar morphology. A definitive diagnosis was not rendered due to limited tissue. The case was discussed with the treating surgeon, and excision was recommended with clear margins. Excision of the lesion showed typical ASPS. A TFE-3 immunohistochemical stain was done, which showed strong immunoreactivity, thereby confirming the diagnosis of ASPS. This tumour is rare, and its presence in the tongue makes it extremely infrequent.
摘要：
肺泡软组织肉瘤（ASPS）是一种罕见的软组织肉瘤，通常影响青少年和年轻人，它可以发生在任何年龄。我们报告了一例舌头的ASPS,这在这个地方非常罕见。患者舌头上出现息肉状病变，活检显示颗粒状和肺泡形态。由于组织有限，未做出明确诊断。与主治医生讨论了这个病例,建议切除边缘清晰。病灶切除显示典型的ASPS。进行了TFE-3免疫组织化学染色，表现出强烈的免疫反应性，从而确认ASPS的诊断。这个肿瘤很罕见,它在舌头上的存在使它非常罕见。
