Abstract：
Primary adrenal angiosarcomas are exceedingly rare with a rapidly progressive clinical course and a poor outcome. Establishing the diagnosis can be challenging, and it is complicated by the fact that there are no characteristic clinical or imaging features that are pathognomonic for angiosarcoma. Histologically, they can overlap with other more commonly encountered adrenal tumors. Herein, we present an otherwise healthy 41-year-old woman diagnosed with a primary adrenal epithelioid angiosarcoma. We aim to expand the knowledge of the sparse literature existing on primary adrenal angiosarcomas to help better understand the diagnostic features, clinical behavior, and management of these rare tumors.
摘要：
原发性肾上腺血管肉瘤极为罕见，临床病程进展迅速，预后不良。建立诊断可能具有挑战性，而且，由于没有特征性的临床或影像学特征是血管肉瘤的病理特征，这一事实使情况变得复杂。组织学上,它们可以与其他更常见的肾上腺肿瘤重叠。在这里，我们介绍了一名41岁健康的女性，她被诊断为原发性肾上腺上皮样血管肉瘤。我们的目标是扩大现有的关于原发性肾上腺血管肉瘤的稀疏文献的知识，以帮助更好地理解诊断特征，临床行为，以及这些罕见肿瘤的治疗。
