关键词: ambiguous genitalia gonadal dysgenesis hermaphrodite ovotestis vaginectomy

来  源:   DOI:10.7759/cureus.40104   PDF(Pubmed)

Abstract:
A case is reported herein of a true hermaphrodite (TH) with an ovotestis, a uterus, a vagina, and an underdeveloped phallus. The patient was raised by his parents as a male, based on the presence of a phallus with ambiguous genitalia. He started experiencing breast enlargement at the age of 14 and menarche by the age of 17. He was reviewed using ultrasound, magnetic resonance imaging of the abdomen, and karyotyping, and the reports showed evidence of Mullerian structures and 46 XX karyotyping. Based on the preferences of the patient and his parents and their psychological outlook toward the male gender, a total mastectomy, hysterectomy, bilateral gonadectomy, and total vaginectomy were performed. This was followed by reconstruction of the male genitalia and supplemented with male hormone replacement therapy. Accordingly, a TH was assigned a male gender.
摘要:
本文报道了一例真雌雄同体(TH),子宫,一个阴道,和不发达的阳具。病人是由他的父母抚养长大的男性,基于生殖器模棱两可的阴茎的存在。他从14岁开始经历乳房增大,到17岁开始初潮。他接受了超声波检查,腹部磁共振成像,和核型分析,报告显示了Mullerian结构和46XX核型的证据。根据患者及其父母的偏好以及他们对男性性别的心理看法,全乳房切除术,子宫切除术,双侧性腺切除术,进行全阴道切除术。随后是男性生殖器的重建,并辅以男性激素替代疗法。因此,TH被分配为男性。
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