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Abstract：
Syringocystadenocarcinoma papilliferum (SCACP) is an exceptionally rare cutaneous adnexal tumor that is infrequently encountered by clinicians worldwide. The tumor typically appears in the older population, affecting patients in their fifth and sixth decades of life without male or female predominance. Patients frequently present with a variable-sized hyperpigmented ulcerative lesion containing an exudate that has a long-standing course of progression from its benign counterpart, Syringocystadenoma papilliferum (SCAP). Additionally, the clinical presentation and morphology of the neoplasm can be easily confused with a variety of other skin cancers, such as squamous cell carcinoma (SCC), basal cell carcinoma (BCC), cutaneous lymphoma, and cutaneous metastasis. Therefore, histopathology and tissue analysis play an essential role in establishing an accurate diagnosis. However, the lesion is so rare that no definitive diagnostic markers have been established yet. We present a case of SCACP localized to the scalp of the patient. Our case study highlights the presence of specific tumor markers that could potentially serve as objective criteria for diagnosis.
摘要：
视神经囊腺癌乳头瘤（SCACP）是一种极为罕见的皮肤附件肿瘤，全世界的临床医生都很少遇到。肿瘤通常出现在老年人群中，影响患者在他们的第五和六十年的生活没有男性或女性为主。患者经常表现为可变大小的色素沉着型溃疡性病变，其中包含从良性对应物开始长期进展的渗出物，乳头状视神经囊腺瘤（SCAP）。此外,肿瘤的临床表现和形态很容易与各种其他皮肤癌混淆，例如鳞状细胞癌（SCC），基底细胞癌（BCC），皮肤淋巴瘤,和皮肤转移。因此,组织病理学和组织分析在建立准确的诊断中起着至关重要的作用。然而,病变非常罕见，尚未建立明确的诊断标记物。我们介绍了一例位于患者头皮的SCACP病例。我们的案例研究强调了可能作为诊断客观标准的特定肿瘤标志物的存在。
