PDF(Pubmed)
Abstract：
Desmoid tumors are rare. They account for roughly 0.03% of all neoplasms and less than 3% of all soft tissue tumors. They are locally aggressive tumors with no known metastatic potential or dedifferentiation. A 29-year-old woman with no family history of neoplasms presented with a mass in the cervical region and moderate pain that had developed a year before. The patient underwent marginal resection of the bilateral posterior and lateral compartments of the neck. The histopathological report confirmed the diagnosis of desmoid tumor with nuclear positivity for beta-catenin. The patient received radiotherapy but did not show a favorable response; she has stable disease and takes colchicine at one-year follow-up.
摘要：
纤维瘤很少见。它们约占所有肿瘤的0.03％，占所有软组织肿瘤的不到3％。它们是局部侵袭性肿瘤，没有已知的转移潜力或去分化。一名29岁的妇女，没有肿瘤家族史，表现为宫颈区域肿块和一年前出现的中度疼痛。患者接受了颈部双侧后部和外侧区室的边缘切除术。组织病理学报告证实了对β-catenin的核阳性的硬纤维瘤的诊断。患者接受了放疗，但没有表现出良好的反应；她病情稳定，在一年的随访中服用秋水仙碱。
