PDF(Pubmed)
Abstract：
UNASSIGNED: Vagal paragangliomas of neck are rare tumours of neural crest origin usually arising in elderly age with female predominance. They have a vague clinical presentation therefore difficult to diagnose preoperatively. We hope that this case report and literature review would add to the existing literature and help devise a comprehensive diagnostic and therapeutic plan for vagal paragangliomas.
METHODS: We report a case of vagal paraganglioma occurring in a 13-year-old male which is an extremely rare presentation in this age group. The patient presented with a large solitary painless progressively growing mass in posterior triangle of neck. External jugular vein was stretched and trachea was deviated medially. The mass was arising via a twig from vagus nerve and was surgically excised. Diagnosis was established post-operatively through histopathological analysis.
UNASSIGNED: Vagal paraganglioma is a rare occurrence in male teenagers and may mimic schwannoma, neuroma, jugular meningioma, or other gangliomas. Surgical excision is mainstay of treatment but resultant vagal complications and neurological consequences are usually unavoidable. Nonetheless, the prognosis may be easily improved with sound surgical judgement, skill, and routine follow-up.
CONCLUSIONS: Vagal paraganglioma usually presents as a swelling in neck and cannot be diagnosed on simple clinical examination. CT scan and MRI are imaging modalities of choice and can be coupled with angiography to increase diagnostic accuracy. Although both radiation therapy and surgical excision have both been found to be successful treatment options, it is still unclear which is more beneficial.
METHODS: We report a case of vagal paraganglioma occurring in a 13-year-old male which is an extremely rare presentation in this age group. The patient presented with a large solitary painless progressively growing mass in posterior triangle of neck. External jugular vein was stretched and trachea was deviated medially. The mass was arising via a twig from vagus nerve and was surgically excised. Diagnosis was established post-operatively through histopathological analysis.
UNASSIGNED: Vagal paraganglioma is a rare occurrence in male teenagers and may mimic schwannoma, neuroma, jugular meningioma, or other gangliomas. Surgical excision is mainstay of treatment but resultant vagal complications and neurological consequences are usually unavoidable. Nonetheless, the prognosis may be easily improved with sound surgical judgement, skill, and routine follow-up.
CONCLUSIONS: Vagal paraganglioma usually presents as a swelling in neck and cannot be diagnosed on simple clinical examination. CT scan and MRI are imaging modalities of choice and can be coupled with angiography to increase diagnostic accuracy. Although both radiation therapy and surgical excision have both been found to be successful treatment options, it is still unclear which is more beneficial.
摘要：
■颈部迷走神经节旁瘤是罕见的神经嵴起源肿瘤，通常发生在老年，女性为主。它们的临床表现模糊，因此术前难以诊断。我们希望此病例报告和文献综述将增加现有文献，并有助于为迷走神经节旁瘤制定全面的诊断和治疗计划。
方法：我们报告一例发生在一名13岁男性的迷走神经节旁瘤，这在该年龄组中极为罕见。该患者在颈部后三角形表现出巨大的单发无痛逐渐增长的肿块。颈外静脉拉伸，气管内侧偏斜。肿块是通过迷走神经的细枝产生的，并通过手术切除。术后通过组织病理学分析确定诊断。
■迷走神经副神经节瘤在男性青少年中很少见，可能模仿神经鞘瘤，神经瘤,颈静脉脑膜瘤,或其他神经节瘤。手术切除是治疗的主要手段，但随之而来的迷走神经并发症和神经系统后果通常是不可避免的。尽管如此，通过良好的手术判断，预后可能很容易改善，技能，和常规随访。
结论：迷走神经副神经节瘤通常表现为颈部肿胀，不能通过简单的临床检查诊断。CT扫描和MRI是首选的成像方式，可以与血管造影结合使用以提高诊断准确性。尽管放射治疗和手术切除都被发现是成功的治疗选择，尚不清楚哪个更有益。
方法：我们报告一例发生在一名13岁男性的迷走神经节旁瘤，这在该年龄组中极为罕见。该患者在颈部后三角形表现出巨大的单发无痛逐渐增长的肿块。颈外静脉拉伸，气管内侧偏斜。肿块是通过迷走神经的细枝产生的，并通过手术切除。术后通过组织病理学分析确定诊断。
■迷走神经副神经节瘤在男性青少年中很少见，可能模仿神经鞘瘤，神经瘤,颈静脉脑膜瘤,或其他神经节瘤。手术切除是治疗的主要手段，但随之而来的迷走神经并发症和神经系统后果通常是不可避免的。尽管如此，通过良好的手术判断，预后可能很容易改善，技能，和常规随访。
结论：迷走神经副神经节瘤通常表现为颈部肿胀，不能通过简单的临床检查诊断。CT扫描和MRI是首选的成像方式，可以与血管造影结合使用以提高诊断准确性。尽管放射治疗和手术切除都被发现是成功的治疗选择，尚不清楚哪个更有益。
