PDF(Pubmed)
Abstract：
Moyamoya disease is a rare cerebrovascular disorder characterized by progressive stenosis and occlusion of the intracranial arteries, resulting in the formation of collateral vessels. We present a case of a 24-year-old South Asian female with no prior medical history who presented with persistent headaches, right-hand numbness and pain, and global aphasia. Imaging revealed severe steno-occlusive disease involving the left internal carotid artery terminus, the proximal middle cerebral artery (MCA), and the anterior cerebral artery. The patient underwent a hemicraniectomy due to malignant MCA syndrome and was prescribed aspirin and fluoxetine. Further evaluation with a cerebral angiogram revealed severe steno-occlusive disease involving the left internal carotid artery terminus, the proximal middle cerebral artery, and the anterior cerebral artery. The patient had Moyamoya disease. This case emphasizes the necessity of including Moyamoya disease in the differential diagnosis, as it can result in serious neurological impairments.
摘要：
烟雾病是一种罕见的脑血管疾病，其特征是颅内动脉进行性狭窄和闭塞，导致侧支血管的形成。我们介绍了一名24岁的南亚女性，没有既往病史，患有持续性头痛，右手麻木和疼痛，和全球性失语症。影像学显示严重狭窄闭塞性疾病累及左侧颈内动脉末端，大脑中动脉(MCA)近端,还有大脑前动脉.由于恶性MCA综合征，患者接受了半切除术，并服用了阿司匹林和氟西汀。用脑血管造影进一步评估显示涉及左颈内动脉末端的严重狭窄闭塞性疾病，大脑中动脉近端,还有大脑前动脉.患者患有烟雾病。该病例强调了将烟雾病纳入鉴别诊断的必要性，因为它会导致严重的神经损伤。
