关键词: COVID-19 X-linked agammaglobulinemia computed tomography migrant pneumonia organizing pneumonia

Mesh : Humans COVID-19 / complications Pneumonia Genetic Diseases, X-Linked Agammaglobulinemia / complications diagnostic imaging

来  源:   DOI:10.3390/tomography9030073   PDF(Pubmed)

Abstract:
X-linked agammaglobulinemia (XLA) is a primary immunodeficiency characterized by marked reduction in serum immunoglobulins and early-onset infections. Coronavirus Disease-2019 (COVID-19) pneumonia in immunocompromised patients presents clinical and radiological peculiarities which have not yet been completely understood. Very few cases of agammaglobulinemic patients with COVID-19 have been reported since the beginning of the pandemic in February 2020. We report two cases of migrant COVID-19 pneumonia in XLA patients.
摘要:
X连锁无丙种球蛋白血症(XLA)是一种原发性免疫缺陷,其特征是血清免疫球蛋白和早发性感染显着减少。免疫功能低下患者的冠状病毒病-2019(COVID-19)肺炎呈现临床和放射学特性,尚未完全了解。自2020年2月大流行开始以来,报告的COVID-19无球蛋白血症患者病例很少。我们报告了两例XLA患者的移民COVID-19肺炎。
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