PDF(Pubmed)
Abstract：
Myxofibrosarcoma (MFS) is a soft tissue sarcoma that commonly occurs in late adult life. It is mainly located in the subcutaneous soft tissues of extremities characterized by a high recurrence rate at the original site. MFS of the head and neck is rare, while it occurrence in the maxilla is extremely rare. We report an atypical case of MFS of the maxilla in a 29-year-old male. The tumour was resected with adequate margin and following which post-operative adjuvant radiotherapy was given. This patient has been followed for 2 years to date and has remained disease free. The rarity, the aggressive nature of the pathology, the extent of the tumour and the complex neurovascular structures in close proximity to the site often lead to adverse outcomes. We will be discussing a rare case of a rapidly growing high grade maxillary sinus MFS in a young patient with a history of radiation exposure which posed as a diagnostic challenge. Our case may provide additional diagnostic and treatment experience with regards to managing maxillary sinus myxofibrosarcoma.
摘要：
粘液纤维肉瘤（MFS）是一种软组织肉瘤，通常发生在成年后期。它主要位于四肢的皮下软组织中，其特征在于原始部位的高复发率。头部和颈部的MFS很少见，而它在上颌骨的发生极为罕见。我们报告了一名29岁男性上颌骨MFS的非典型病例。切除肿瘤的边缘足够，随后进行术后辅助放疗。到目前为止，该患者已经被随访了2年，并且一直没有疾病。稀有，病理学的侵略性，肿瘤的范围和靠近该部位的复杂神经血管结构通常会导致不良后果。我们将讨论一例罕见的病例，该病例是一名年轻的患者，该患者有辐射暴露史，这对诊断提出了挑战。我们的病例可能会为管理上颌窦粘液纤维肉瘤提供更多的诊断和治疗经验。
