Abstract:
We describe a case of segmental arterial mediolysis (SAM) in a 2-year-old male who presented with symptoms of acute pancreatitis. SAM is a vascular entity of unknown etiology that involves medium-sized arteries in which the integrity of the vessel wall is compromised, resulting in increased susceptibility to ischemia, hemorrhage, and dissection. The clinical presentation is variable and can range from abdominal pain to more ominous findings of abdominal hemorrhage or organ infarction. This entity should be considered in the correct clinical setting and after other vasculopathies have been excluded. We aim to bring awareness to pediatric providers given this is a rare entity with variable presentation, which could be potentially life threatening.
摘要:
我们描述了一名2岁男性出现急性胰腺炎症状的节段性动脉介质溶解(SAM)病例。SAM是一种病因不明的血管实体,涉及中等大小的动脉,其中血管壁的完整性受到损害。导致对缺血的易感性增加,出血,和解剖。临床表现是可变的,从腹痛到更不祥的腹腔出血或器官梗塞。应在正确的临床环境中以及排除其他血管病变后考虑此实体。我们的目标是让意识到儿科提供者,因为这是一个罕见的实体,具有可变的表现,这可能会危及生命。