PDF(Pubmed)
Abstract：
Herlyn-Werner-Wunderlich syndrome (HWWS) is a rare developmental anomaly of the female reproductive system caused by a failure of fusion during Mullerian duct development. The triad of uterus didelphys, obstructed hemivagina, and ipsilateral renal agenesis characterizes HWWS. The most common presenting symptoms are dysmenorrhoea, pelvic pain, primary infertility in later years, and an abdominal mass due to hematometrocolpos.
UNASSIGNED: A 17-year-old girl presented to the authors\' department with recurrent low back pain, which was neither responsive to analgesics nor associated with urinary complaints, vomiting, or fever. Imaging techniques confirmed she had the triad of uterus didelphys, obstructed hemivagina, and right renal agenesis.
UNASSIGNED: The genital system is the same for males and females before 6 weeks of pregnancy. HWWS is a rare congenital disorder as a result of the failure of fusion during Mullerian duct development. It consists of a didelphic uterus, hemivaginal septum, and unilateral renal agenesis.
UNASSIGNED: Shame and social stigma associated with virginity continue to endanger the lives of many girls in Syria. To complicate matters further, the low resources in Syria produced by war pose a difficult challenge in managing many gynecological conditions, including HWWS, like this case, in which endoscopic technologies were not available, necessitating open surgery while keeping in mind preserving hymen intactness. So, the authors indicate that preserving virginity could be conducted even though the approach is open surgery by very careful intervention and experienced surgeons.
UNASSIGNED: A 17-year-old girl presented to the authors\' department with recurrent low back pain, which was neither responsive to analgesics nor associated with urinary complaints, vomiting, or fever. Imaging techniques confirmed she had the triad of uterus didelphys, obstructed hemivagina, and right renal agenesis.
UNASSIGNED: The genital system is the same for males and females before 6 weeks of pregnancy. HWWS is a rare congenital disorder as a result of the failure of fusion during Mullerian duct development. It consists of a didelphic uterus, hemivaginal septum, and unilateral renal agenesis.
UNASSIGNED: Shame and social stigma associated with virginity continue to endanger the lives of many girls in Syria. To complicate matters further, the low resources in Syria produced by war pose a difficult challenge in managing many gynecological conditions, including HWWS, like this case, in which endoscopic technologies were not available, necessitating open surgery while keeping in mind preserving hymen intactness. So, the authors indicate that preserving virginity could be conducted even though the approach is open surgery by very careful intervention and experienced surgeons.
摘要：
Herlyn-Werner-Wunderlich综合征（HWWS）是由于穆勒导管发育过程中融合失败而引起的女性生殖系统罕见的发育异常。子宫的三合会，阻塞的半阴道,同侧肾发育不全是HWWS的特征。最常见的症状是痛经，盆腔疼痛,原发性不孕症在以后几年，以及因血吸虫引起的腹部肿块.
■一位17岁的女孩因反复出现的腰痛出现在作者部门，对镇痛药既无反应，也与泌尿系不适有关，呕吐,或发烧。成像技术证实她患有子宫双子宫三联征，阻塞的半阴道,和右肾发育不全。
■男性和女性在怀孕6周前的生殖系统是相同的。HWWS是一种罕见的先天性疾病，是在穆勒管发育过程中融合失败的结果。它由一个双形子宫组成，半阴道隔,和单侧肾脏发育不全.
■与童贞相关的耻辱和社会污名继续危及叙利亚许多女孩的生命。使事情进一步复杂化，叙利亚因战争而产生的资源不足，对管理许多妇科疾病构成了艰巨的挑战，包括HWWS,就像这个案子,在没有内窥镜技术的情况下，需要进行开放手术，同时牢记处女膜的完整性。所以,作者指出，即使该方法是由非常仔细的干预和经验丰富的外科医生进行的开放式手术，也可以进行处女。
■一位17岁的女孩因反复出现的腰痛出现在作者部门，对镇痛药既无反应，也与泌尿系不适有关，呕吐,或发烧。成像技术证实她患有子宫双子宫三联征，阻塞的半阴道,和右肾发育不全。
■男性和女性在怀孕6周前的生殖系统是相同的。HWWS是一种罕见的先天性疾病，是在穆勒管发育过程中融合失败的结果。它由一个双形子宫组成，半阴道隔,和单侧肾脏发育不全.
■与童贞相关的耻辱和社会污名继续危及叙利亚许多女孩的生命。使事情进一步复杂化，叙利亚因战争而产生的资源不足，对管理许多妇科疾病构成了艰巨的挑战，包括HWWS,就像这个案子,在没有内窥镜技术的情况下，需要进行开放手术，同时牢记处女膜的完整性。所以,作者指出，即使该方法是由非常仔细的干预和经验丰富的外科医生进行的开放式手术，也可以进行处女。
