Abstract：
Dural sinus malformations (DSMs) are rare congenital vascular diseases characterized by a giant venous pouch with or without arteriovenous shunts. We present a neonatal case of DSM that was diagnosed prenatally and treated via endovascular intervention in the early postnatal period. The patient presented with a large DSM involving the torcular Herophilion prenatal magnetic resonance imaging (MRI). Enlargement of the head circumference and respiratory failure rapidly progressed after birth. On the 5th day after birth, the neonate underwent endovascular occlusion via the umbilical artery. The arteriovenous shunt was occluded, and the reflux from the enlarged venous pouch to the dural sinus was decreased. No additional procedure other than ventriculoperitoneal shunting was required. The neonate\'s development slowly caught up to normal parameters. Follow-up MRI demonstrated the successful development of the venous drainage system. DSMs are characterized by an abnormally dilated dural sinus, which can block the venous return and ultimately increase intracranial pressure and cerebral ischemia. Long-term follow-up indicates that an abnormally developed dural sinus can be reconstructed by appropriate and timely treatment.
摘要：
硬脑膜窦畸形（DSMs）是罕见的先天性血管疾病，其特征是有或没有动静脉分流的巨大静脉袋。我们介绍了一例DSM的新生儿病例，该病例是在产前诊断的，并在出生后早期通过血管内介入治疗。患者出现大型DSM，涉及环形Herophilion产前磁共振成像（MRI）。出生后头围增大和呼吸衰竭迅速发展。出生后第5天,新生儿经脐动脉血管内闭塞.动静脉分流阻塞,从扩大的静脉囊到硬脑膜窦的回流减少。除脑室腹膜分流术外，不需要其他手术。新生儿的发育慢慢赶上正常参数。随访MRI证明了静脉引流系统的成功开发。DSM的特征是硬脑膜窦异常扩张，可以阻断静脉回流，最终增加颅内压和脑缺血。长期随访表明，通过适当和及时的治疗可以重建异常发育的硬脑膜窦。
