PDF(Pubmed)
Abstract：
Anomalous origin of the left pulmonary artery from the descending aorta is an extremely rare congenital malformation. There were merely four case reports of such malformation in previous literature, and all four cases underwent surgical repair in their first year of life. Actually, long-term pulmonary arterial hypertension and irreversible pulmonary vascular changes make anesthesia management quite a challenge, while anesthesia for managing these cases has not been discussed before. We present a 15-year-old boy undergoing corrective surgery and try to provide some tips on anesthesia management for this surgical procedure. Through optimal perioperative management, successful outcomes can be achieved for this malformation.
摘要：
左肺动脉异常起源于降主动脉是一种极为罕见的先天性畸形。在以前的文献中只有四例这种畸形的报道，所有四例在生命的第一年都接受了手术修复。事实上,长期的肺动脉高压和不可逆的肺血管变化使麻醉管理面临相当大的挑战，虽然以前没有讨论过管理这些病例的麻醉。我们介绍了一个正在接受矫正手术的15岁男孩，并尝试为该手术提供一些麻醉管理技巧。通过优化围手术期管理，这种畸形可以取得成功的结果。
