Abstract:
Jugular foramen tumours are uncommon, deeply located, and eloquently situated, making their diagnosis and management challenging. Paragangliomas and other benign tumours comprise the large majority of lesions in this region, but malignant tumours are occasionally identified. We report a unique case of a solitary plasmacytoma of the jugular foramen resembling a jugulotympanic paraganglioma. A solitary plasmacytoma of the jugular foramen is both rare in location and in disease presentation, as most plasma cell neoplasms are diagnosed as multiple myeloma. Our 75-year-old patient presented with symptoms typical for a jugular foramen tumour. Although there are radiographic features which help differentiate paragangliomas from other benign and malignant tumours, plasmacytomas are highly vascular and can demonstrate a local infiltrative spread which can mimic the radiographic appearance of a paraganglioma. Clinicians should consider plasma cell neoplasms in the differential when faced with an unusual presentation of a jugular foramen lesion. Our patient was treated with definitive radiotherapy to 45 Gy, which was very effective local treatment for the solitary plasmacytoma.
摘要:
颈静脉孔肿瘤并不常见,深深的位置,雄辩地位于,使他们的诊断和管理具有挑战性。副神经节瘤和其他良性肿瘤构成了该区域的大部分病变,但偶尔会发现恶性肿瘤。我们报告了一个独特的病例,类似于颈静脉鼓室副神经节瘤的颈静脉孔孤立性浆细胞瘤。颈静脉孔的孤立性浆细胞瘤在位置和疾病表现上都很少见。因为大多数浆细胞肿瘤被诊断为多发性骨髓瘤。我们的75岁患者出现颈静脉孔肿瘤的典型症状。尽管有影像学特征有助于区分副神经节瘤与其他良性和恶性肿瘤,浆细胞瘤是高度血管化的,可以表现出局部浸润性扩散,可以模仿副神经节瘤的影像学表现。当面对颈静脉孔病变的异常表现时,临床医生应考虑浆细胞肿瘤的差异。我们的病人接受了45Gy的明确放疗,这是孤立性浆细胞瘤的非常有效的局部治疗。