Abstract：
A 6-year-old girl presented with moderate-intensity headache, frequent vomiting, visual disturbance, and left-sided decreased hearing for 7 months. The neurologic examination revealed a right upper motor neuron facial nerve palsy, left-sided 4-mm sluggish pupil (right: 3-mm reactive), and unsteady gait. Fundoscopy was notable for bilateral papilledema. Brain magnetic resonance imaging with contrast demonstrated a giant multiloculated suprasellar cystic lesion (9.7 × 10.5 × 7.6 cm). It extended to the left anterior cranial fossa, both middle cranial fossae, and posterior fossa prepontine region with consequent effect on the brainstem and moderate hydrocephalus. The patient underwent a right frontal external ventricular drain insertion and left frontotemporal craniotomy and tumor resection. Histopathologic sections were compatible with adamantinomatous craniopharyngioma. Giant craniopharyngiomas have rarely been reported. This article presents the clinical and radiologic outcomes of a patient with a giant craniopharyngioma.
摘要：
一名6岁女孩出现中等强度头痛，频繁呕吐,视觉障碍,左侧听力下降7个月。神经系统检查显示右上运动神经元面神经麻痹，左侧4毫米缓慢瞳孔（右：3毫米反应性），和不稳定的步态。眼底镜检查可见双侧乳头水肿。增强脑磁共振成像显示巨大的多部位鞍上囊性病变（9.7×10.5×7.6cm）。它延伸到左前颅窝，两个中颅窝，后颅窝脑前区对脑干和中度脑积水有影响。患者接受了右额外室引流插入和左额颞部开颅手术和肿瘤切除术。组织病理学切片与菱形颅咽管瘤相容。很少报道巨大的颅咽管瘤。本文介绍了患有巨大颅咽管瘤的患者的临床和放射学结果。
