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Abstract：
BACKGROUND: This article examines primary hepatic angiosarcoma (PHA) and fat-poor angiomyolipoma (AML), two uncommon vascular cancers. Clinical decisions in these situations are frequently aided by pathology reports and imaging techniques. Uncommon malignant tumors of the vascular endothelium include PHA. Another diagnosis that should not be overlooked when employing contrast-enhanced MR and contrast-enhanced computed tomography (CT) imaging techniques is fat-poor AML, one of the uncommon vascular tumors of the liver. In both conditions, biopsy is the primary means of diagnosis.
METHODS: In our article, besides the diagnosis of PHA, fat-poor AML, one of the other rare vascular tumors of the liver, is mentioned. In the case, a 50-year-old female patient with VHL Syndrome was admitted to our hospital with nonspecific lesions such as right upper quadrant pain, weight loss, and nausea. Abdominal ultrasonography (US) revealed a hypoechoic heterogeneous lesion with occasional faint contours. In computed tomography, it was observed as a hyperdense nodular lesion in segment 4. Magnetic resonance imaging (MRI) revealed that the lesion did not contain fat. In connection with the known history of VHL Syndrome, we first evaluated the possibility of AML. Thereupon, a histopathological sample was taken and the diagnosis was made as fat-poor AML with 5% fat content.
CONCLUSIONS: In conclusion, PHA in our case report and fat-poor AML in our clinic are two uncommon liver vascular malignancies with comparable incidences. Important imaging techniques like contrast-enhanced US (CEUS), CECT, and CEMRI give us substantial advantages in both cases. However, a biopsy is used to provide the final diagnosis.
METHODS: In our article, besides the diagnosis of PHA, fat-poor AML, one of the other rare vascular tumors of the liver, is mentioned. In the case, a 50-year-old female patient with VHL Syndrome was admitted to our hospital with nonspecific lesions such as right upper quadrant pain, weight loss, and nausea. Abdominal ultrasonography (US) revealed a hypoechoic heterogeneous lesion with occasional faint contours. In computed tomography, it was observed as a hyperdense nodular lesion in segment 4. Magnetic resonance imaging (MRI) revealed that the lesion did not contain fat. In connection with the known history of VHL Syndrome, we first evaluated the possibility of AML. Thereupon, a histopathological sample was taken and the diagnosis was made as fat-poor AML with 5% fat content.
CONCLUSIONS: In conclusion, PHA in our case report and fat-poor AML in our clinic are two uncommon liver vascular malignancies with comparable incidences. Important imaging techniques like contrast-enhanced US (CEUS), CECT, and CEMRI give us substantial advantages in both cases. However, a biopsy is used to provide the final diagnosis.
摘要：
背景：本文检查了原发性肝血管肉瘤（PHA）和脂肪贫乏的血管平滑肌脂肪瘤（AML），两种罕见的血管癌.在这些情况下的临床决策通常由病理报告和成像技术来辅助。不常见的血管内皮恶性肿瘤包括PHA。采用对比增强MR和对比增强计算机断层扫描（CT）成像技术时，另一个不应忽视的诊断是脂肪贫乏的AML，肝脏罕见的血管瘤之一。在这两种情况下，活检是诊断的主要手段。
方法：在我们的文章中，除了PHA的诊断，脂肪贫乏的AML，另一种罕见的肝脏血管瘤，提到了。在案件中,一名50岁的女性VHL综合征患者因右上腹疼痛等非特异性病变入院，减肥,和恶心。腹部超声检查（US）显示低回声异质性病变，偶尔有模糊的轮廓。在计算机断层扫描中，在第4段观察到为高密度结节性病变。磁共振成像（MRI）显示病变不含脂肪。关于已知的VHL综合征病史，我们首先评估了AML的可能性。于是,采集组织病理学样本,诊断为脂肪含量为5%的贫脂AML.
结论：结论：我们的病例报告中的PHA和我们诊所中的脂肪贫乏的AML是两种罕见的肝血管恶性肿瘤，发病率相当。重要的成像技术，如对比增强US（CEUS），CECT,在这两种情况下，CEMRI都给我们带来了巨大的优势。然而,活检用于提供最终诊断。
方法：在我们的文章中，除了PHA的诊断，脂肪贫乏的AML，另一种罕见的肝脏血管瘤，提到了。在案件中,一名50岁的女性VHL综合征患者因右上腹疼痛等非特异性病变入院，减肥,和恶心。腹部超声检查（US）显示低回声异质性病变，偶尔有模糊的轮廓。在计算机断层扫描中，在第4段观察到为高密度结节性病变。磁共振成像（MRI）显示病变不含脂肪。关于已知的VHL综合征病史，我们首先评估了AML的可能性。于是,采集组织病理学样本,诊断为脂肪含量为5%的贫脂AML.
结论：结论：我们的病例报告中的PHA和我们诊所中的脂肪贫乏的AML是两种罕见的肝血管恶性肿瘤，发病率相当。重要的成像技术，如对比增强US（CEUS），CECT,在这两种情况下，CEMRI都给我们带来了巨大的优势。然而,活检用于提供最终诊断。
