Abstract：
Among persons with neuromuscular mobility limitations, therapeutic positioning has been implemented to improve body function, avoid secondary complications such as contractures and body shape distortions, and optimize body energy through restorative sleep. This case study describes the application of a 24-hour posture care management intervention for a preadolescent girl with Aicardi syndrome. The intervention was administered by adding therapeutic bed positioning to use of a custom molded wheelchair seating system. Over the 6-year intervention period overlapping with the subject\'s adolescent years (age 11-17), marked improvement was observed in thoracic shape and symmetry. Moreover, the subject\'s mother reported regular full-nights of uninterrupted sleep, relaxed muscle tone upon waking, a stronger cough with less audible congestion, more efficient swallowing and zero hospitalizations. The 24-hour posture care management intervention offers an alternative option for families and caregivers of persons with neuromuscular mobility impairments who wish to use a low-risk, noninvasive, locally available approach to improve body symmetry, increase hours of restorative sleep, and ease caregiving routines. Further research in 24-hour posture care management, including positioning for sleep and rest, should be explored in individuals with complex movement limiting disabilities who are at risk of developing neuromuscular scoliosis.
摘要：
在神经肌肉活动受限的人中，治疗定位已经实施，以改善身体功能，避免继发性并发症，如挛缩和体形扭曲，通过恢复性睡眠优化身体能量。本案例研究描述了24小时姿势护理管理干预在患有Aicardi综合征的青春期前女孩中的应用。通过在使用定制模制轮椅座椅系统的基础上添加治疗床定位来进行干预。在与受试者的青春期（11-17岁）重叠的6年干预期内，在胸廓形状和对称性方面观察到明显改善。此外，受试者的母亲报告有规律的整晚不间断的睡眠，醒来时肌肉张力放松，咳嗽更强，充血更少，更有效的吞咽和零住院。24小时姿势护理管理干预为希望使用低风险神经肌肉活动障碍患者的家庭和护理人员提供了另一种选择，非侵入性，本地可用的方法来改善身体对称性，增加恢复性睡眠的时间，放松护理程序。24小时姿势护理管理的进一步研究，包括睡眠和休息的定位，对于有发生神经肌肉脊柱侧凸风险的复杂运动限制性残疾患者,应进行探讨.
