Abstract:
Mature fetiform teratoma, or homunculus, is a term coined for a rare variant of teratoma with a prevalence of 0.01% of teratomas. There have been very few cases reported in the world, and its thoracic presentation is extremely unusual. We present the case of a 31-year-old female patient with a history of progressive chest pain in the left hemithorax, associated with dyspnea on moderate exertion and cough. Imaging studies revealed a large intrathoracic tumor visually compatible with a teratoma. Surgical resection by a clamshell approach was successful, and subsequent anatomopathological studies of the operative specimen concluded that the mass was a mature fetiform thoracic teratoma. The treatment of this entity is generally surgical and includes wide resection due to its large adhesive component to surrounding tissues. Thus, the cardiothoracic surgeon must know approaches that allow wide resection, making these cases true surgical challenges.
摘要:
成熟外形畸胎瘤,或者长尾猴,是畸胎瘤的罕见变种的术语,畸胎瘤的患病率为0.01%。世界上报道的病例很少,它的胸部表现非常不寻常。我们介绍了一个31岁的女性患者,在左半胸有进行性胸痛的病史,伴有中度劳累和咳嗽的呼吸困难。影像学检查显示,在视觉上与畸胎瘤相容的胸内大肿瘤。蛤壳式手术切除是成功的,随后对手术标本进行的解剖病理学研究得出的结论是,该肿块是成熟的鳞片状胸畸胎瘤。该实体的治疗通常是手术的,并且由于其与周围组织的大粘附成分而包括广泛切除。因此,心胸外科医生必须知道允许广泛切除的方法,使这些病例成为真正的手术挑战。