Abstract：
A 33-year-old lady was referred to our clinic with a history of left upper eyelid swelling and difficulty to open her left eye for more than 4 years. Her globe was in infero-nasal displacement, and ocular movement was not full, with restriction to every direction. No clinical sign including eye redness, pain or visual loss was found on examination. Exophthalmometry confirmed 2 mm of left-sided proptosis. Computed tomography (CT) imaging of the orbit obtained in axial and coronal planes depicted an irregular and heterogeneous soft-tissue density mass in the left lacrimal gland, measuring 25 × 17 mm. Magnetic resonance imaging (MRI) revealed the mass of slightly longer T1 and slightly longer/shorter T2 signal, and Gd-enhanced MRI showed a significant enhancement. The tumor was first presumably diagnosed of pleomorphic adenomas. A surgery was applied to remove the tumor completely. Histopathological evaluation led to the diagnosis of PEComa.
摘要：
一位33岁的女士被转诊到我们的诊所，有左上眼睑肿胀的病史，左眼难以睁开超过4年。她的地球仪在鼻下移位，眼球运动不完整，限制每个方向。没有临床症状，包括眼睛发红，检查时发现疼痛或视力丧失。眼球突出术证实左侧突出2mm。在轴向和冠状平面中获得的眼眶的计算机断层扫描（CT）成像描绘了左泪腺中不规则和不均匀的软组织密度肿块，测量25×17毫米。磁共振成像（MRI）显示T1稍长，T2信号稍长/稍短，Gd增强MRI显示明显增强。该肿瘤最初可能被诊断为多形性腺瘤。应用手术以完全切除肿瘤。组织病理学评估导致PEComa的诊断。
