Abstract：
Parturients with vascular Ehlers-Danlos syndrome are at particular risk of hemorrhage, and there is little evidence to guide prevention or management of hemorrhage in these patients. We present the case of a patient with vascular Ehlers-Danlos syndrome who had a cesarean delivery complicated by an intraoperative hemorrhage. Administration of desmopressin and tranexamic acid appeared to be of marked benefit in achieving hemostasis. To the best of our knowledge, this is the first report of the use of desmopressin during major obstetric hemorrhage in vascular Ehlers-Danlos syndrome.
摘要：
患有血管Ehlers-Danlos综合征的产妇特别容易出血，几乎没有证据指导这些患者出血的预防或管理。我们介绍了一例血管性Ehlers-Danlos综合征患者的剖宫产并发术中出血。施用去氨加压素和氨甲环酸似乎在实现止血方面具有显著益处。据我们所知,这是血管性Ehlers-Danlos综合征产科大出血期间使用去氨加压素的首次报道.
