PDF(Pubmed)
Abstract：
Scleromyxedema is an uncommon and progressive fibromucinous disorder characterized by disseminated papular eruption with histological features of dermal mucin deposition. The skin changes associated with this disease are highly visible and they tend to affect the patient\'s quality of life. We report a case of a 50-year-old male patient that presented a 3-year-old history of disseminated asymptomatic firm papules-associated systemic symptoms. Medical treatment with oral corticosteroid and thalidomide was indicated and surgical treatment on residual facial folds was performed, with an excellent outcome.
摘要：
巩膜粘液性水肿是一种罕见的进行性纤维粘液性疾病，其特征是播散性丘疹，具有真皮粘蛋白沉积的组织学特征。与这种疾病相关的皮肤变化非常明显，它们往往会影响患者的生活质量。我们报告了一例50岁的男性患者，该患者有3岁的播散性无症状硬丘疹相关的全身症状史。需要口服皮质类固醇和沙利度胺的药物治疗，并对残留的面部皱褶进行手术治疗。有一个很好的结果。
