PDF(Pubmed)
Abstract：
Cleft palate-lateral synechiae syndrome (CPLSS) is an extremely rare congenital malformation syndrome with undetermined etiology, characterized by a cleft palate and lateral intraoral synechiae linking the free borders of the palate to the mouth floor. We report a case of a female neonate, admitted for suckling difficulties with a cleft lip and palate associated to multiple lateral intraoral synechiae. Resection of the synechiae allowed oral feeding. Cleft palate-lateral synechiae syndrome is an exceptional syndrome as only seventeen cases have been reported in the literature. Synechiae can be isolated or more frequently in association with other congenital anomalies such as cleft lip and/or palate. These synechiae can cause functional deficits, especially in the respiratory and feeding tracts, language disorders or recurrent otitis. Although it is exceptional, this malformative entity must be known by medical practitioners in order to set up a well-adapted therapeutic protocol.
摘要：
腭裂-外侧粘连综合征（CPLSS）是一种极为罕见的先天性畸形综合征，病因不明。其特征是腭裂和口内外侧粘连，将腭的自由边界连接到口腔底。我们报道了一个女性新生儿的病例,因与多个口内外侧粘连相关的唇裂和腭裂而导致的吸乳困难而入院。切除粘连，允许口服喂养。腭裂-外侧粘连综合征是一种特殊综合征，因为文献中仅报道了17例。可以分离或更频繁地与其他先天性异常例如唇裂和/或腭裂相关联。这些粘连会导致功能缺陷，尤其是在呼吸道和呼吸道，语言障碍或复发性中耳炎。虽然是例外,医生必须了解这种畸形实体，才能建立适应良好的治疗方案。
