PDF(Pubmed)
Abstract：
Background: Fibromatosis is a group of benign tumors originating from connective tissues of muscle, overlying fascia, periosteum, or aponeurosis. However, they might need several excisional resections, owing to compressive effects on adjacent vital structures. Case Report: Here, we discussed a case of submandibular fibromatosis in a 3-year-old girl. She underwent a conservative surgical procedure without a wide mandible bone resection. She received no adjuvant therapy. The postoperative period was uneventful with an appropriate cosmetic and functional outcome. A 1-year follow-up revealed no recurrence. Conclusion: Fibromatosis of the head and neck in children is a rare condition, which needs a multidisciplinary agreement for its appropriate management. A complete surgical removal often leads to a proper outcome. Adjuvant therapy should also be kept in mind for recurrent lesions not candidate for surgical removal or in case of remnant tumors.
摘要：
背景：纤维瘤病是一组起源于肌肉结缔组织的良性肿瘤，上覆筋膜,骨膜,或腱膜。然而,他们可能需要多次切除,由于对相邻重要结构的压缩效应。案例报告:这里，我们讨论了一例3岁女孩的颌下纤维瘤病。她接受了保守的外科手术，没有进行广泛的下颌骨切除。她没有接受辅助治疗。术后期间顺利，具有适当的美容和功能结果。1年随访显示无复发。结论：儿童头颈部纤维瘤病是一种罕见的疾病，这需要多学科协议来进行适当的管理。完全的手术切除通常会导致适当的结果。对于不适合手术切除或残留肿瘤的复发性病变，也应牢记辅助治疗。
