POEMS syndrome: A rare cause of ascites and pelvic effusion.

POEMS 综合征 ：腹水和盆腔积液的罕见原因。

• 发表时间: Nov 2022
• 来源期刊: Clin Case Rep
• DOI: 10.1002/ccr3.6603
• PMID: 36408092
• 文章类型: Case Reports
• 作者列表: Ma J,Chen Y,Qin X,Liu X,Li E,Fan H,Xie Y,Wang X

关键词: POEMS syndrome; ascites; case report; hepatosplenomegaly; pelvic effusion; polyneuropathy

Abstract

POEMS syndrome is a rare clonal plasma cell disease associated with multisystem involvement. We reported a case of 48-year-old woman with large volume of exudative ascites with an increased level of λ-light chain and hepatosplenomegaly. The patient was treated with thalidomide and dexamethasone and showed a good clinical response.

摘要

POEMS综合征是一种罕见的与多系统相关的克隆性浆细胞疾病。我们报告了一例48岁女性，伴有大量渗出性腹水，λ轻链水平升高和肝脾肿大。患者接受沙利度胺和地塞米松治疗，临床反应良好。