PDF(Pubmed)
Abstract：
Arrhythmogenic cardiomyopathy is a rare hereditary structural heart disease, with various phenotypes, which mostly affects the right ventricle of the heart, resulting in fibrofatty replacement of the heart muscles and a proclivity to create spontaneous malignant cardiac arrhythmias that may lead to sudden death. Most previous reports were noted on young people. We report a case of its biventricular phenotype in a 61-year-old heavy truck driver who has a current medical history of diabetes mellitus and smoking and was incidentally diagnosed based on the Padua criteria after presenting to the hospital with complaints of lightheadedness and syncope. He eventually had an implantable cardioverter defibrillator, hence preventing death. We were able to correctly diagnose the case and prevent sudden cardiac death by instituting the necessary management.
摘要：
心律失常性心肌病是一种罕见的遗传性结构性心脏病，具有各种表型，主要影响心脏的右心室，导致心肌纤维脂肪替代，并倾向于产生自发性恶性心律失常，可能导致猝死。以前的大多数报告都是关于年轻人的。我们报告了一名61岁的重型卡车司机的双心室表型病例，该司机目前有糖尿病和吸烟史，并在向医院提出头晕和晕厥的投诉后根据帕多瓦标准被偶然诊断。他最终有了植入式心脏复律除颤器，从而防止死亡。通过采取必要的管理措施，我们能够正确诊断病例并预防心脏猝死。
