PDF(Pubmed)
Abstract：
WHAT IS ALREADY KNOWN ABOUT THIS TOPIC?: Epidermolysis bullosa (EB) causes blistering and scarring of the hands resulting in contractures fused web spaces and altered function. Surgery is needed to release contractures and web spaces and hand therapy is essential to maintain results, approaches for both differ. WHAT DOES THIS STUDY ADD?: These guidelines aim to provide information on the surgical and conservative therapeutic hand management of children and adults diagnosed with EB. They are based on available evidence and expert consensus to assist hand surgeons and therapists in decision making, planning and treatment. They highlight the importance of a holistic multidisciplinary team (MDT) approach, where patient priorities are paramount.
摘要：
关于本主题已经知道什么？：大疱性表皮松解症（EB）导致手部起泡和疤痕，导致挛缩融合的网状空间和功能改变。需要手术来释放挛缩和网状空间，而手部治疗对于维持结果至关重要，两者的方法不同。这项研究增加了什么？：这些指南旨在提供有关被诊断为EB的儿童和成人的手术和保守治疗手管理的信息。它们基于现有证据和专家共识，以协助手外科医生和治疗师做出决策，规划和治疗。他们强调了整体多学科团队（MDT）方法的重要性，病人的优先事项是最重要的。
