Abstract：
Malignant peripheral nerve sheath tumour (MPNST) is an aggressive and uncommon cancer developing in the peripheral nerve sheath. Primary cardiac MPNST is an extremely rare finding, with no specific imaging and clinical characteristics. Only a handful of cases have been reported in the literature; thus, little is still known about them. Cardiac computed tomography (CT) and cardiac magnetic resonance imaging (CMRI) are important means of assessing cardiac morphology and function. The preferred course of treatment for this pathology is by full surgical resection of the tumour, with negative (clear) margins, followed by adjuvant radiotherapy and chemotherapy. We present the case of a 42-year-old woman with no significant cardiovascular symptoms who was incidentally diagnosed during routine transthoracic echocardiography (TTE) with a cardiac mass located in the left ventricle.
摘要：
恶性周围神经鞘瘤（MPNST）是在周围神经鞘中发展的侵袭性且罕见的癌症。原发性心脏MPNST是一个极其罕见的发现，没有特定的影像学和临床特征。文献中只报道了少数案例；因此，对他们知之甚少。心脏计算机断层扫描（CT）和心脏磁共振成像（CMRI）是评估心脏形态和功能的重要手段。这种病理的首选治疗方法是对肿瘤进行完全手术切除，具有负(明确)边距，其次是辅助放疗和化疗。我们介绍了一名42岁的女性，该女性没有明显的心血管症状，在常规的经胸超声心动图（TTE）中被偶然诊断为心脏肿块位于左心室。
