Abstract：
Congenital cholesteatoma in identical twins has only been described once in Otolaryngology literature thus far. This report describes a case of monozygotic twins with a history of recurrent acute otitis media and bilateral middle ear effusions without tympanic membrane perforation. Upon myringotomy with pressure equalization tube insertion, both were found to have right-sided cholesteatoma with nearly identical location and pattern of progression. In the context of previous case series demonstrating familial clustering and reports of possible genetic associations of this condition, the authors present an important addition to the current understanding of congenital cholesteatoma disorder.
摘要：
迄今为止，同卵双胞胎中的先天性胆脂瘤在耳鼻咽喉科文献中仅被描述过一次。本报告描述了一例单卵双胞胎，有复发性急性中耳炎和双侧中耳积液而无鼓膜穿孔的病史。在插入压力平衡管的鼓膜切开术中，发现两者均患有右侧胆脂瘤,其位置和进展模式几乎相同.在先前的病例系列中，显示了家族性聚集性，并报告了这种情况的可能遗传关联，作者提出了对目前对先天性胆脂瘤疾病的理解的重要补充。
