Extra-Gastrointestinal Stromal Tumor (EGIST) in the Pelvis Mimicking Retroperitoneal Sarcoma.

骨盆模拟腹膜后肉瘤的胃肠道外间质瘤 （ EGIST ） 。

• 发表时间: Jul 2022
• 来源期刊: Surg J (N Y)
• DOI: 10.1055/s-0042-1757335
• PMID: 36172533
• 文章类型: Case Reports
• 作者列表: El-Helou E,Chamma L,Mazraani HB,Sebaaly D,Chamma OG,Naccour J,Haddad MM,Lichaa D,Alam H,El-Helou E,Chamma L,Mazraani HB,Sebaaly D,Chamma OG,Naccour J,Haddad MM,Lichaa D,Alam H

关键词: GIST; case report; extra-gastrointestinal; retroperitoneal sarcoma; stromal tumors; surgery; GIST; case report; extra-gastrointestinal; retroperitoneal sarcoma; stromal tumors; surgery

Abstract

Extra-gastrointestinal stromal tumors (EGISTs) are rare mesenchymal tumors accounting for less than 1% of total gastrointestinal tumors. They tend to be aggressive and have a poor prognosis. Unfortunately, there is a lack of data or controversial data due to its scarcity. Therefore, we report a case of pelvic EGIST misdiagnosed as retroperitoneal sarcoma. We opted for surgical management followed by adjuvant oral chemotherapy with imatinib.

摘要

胃肠道外间质瘤(EGIST)是罕见的间充质肿瘤,占总胃肠道肿瘤的不到1%。他们往往是积极的，有一个不良的预后。不幸的是,由于其稀缺性，缺乏数据或有争议的数据。因此,我们报告1例盆腔EGIST误诊为腹膜后肉瘤。我们选择了手术治疗，然后用伊马替尼进行辅助口服化疗。