PDF(Pubmed)
Abstract：
Objective We describe the first jugular foramen angiomatoid fibrous histiocytoma (AFH) case and the first treatment with preoperative endovascular embolization. AFH is a rare intracranial neoplasm, primarily found in pediatric patient extremities. With an increase in AFH awareness and a well-described genetic profile, intracranial prevalence has also subsequently increased. Study Design We compare this case to previously reported cases using PubMed/Medline literature search, which was performed using the algorithm [\"intracranial\" AND \"angiomatoid fibrous histiocytoma\"] through December 2020 (23 manuscripts with 46 unique cases). Patient An 8-year-old female presented with failure to thrive and right-sided hearing loss. Work-up revealed an absence of right-sided serviceable hearing and a large jugular foramen mass. Angiogram revealed primary arterial supply from the posterior branch of the ascending pharyngeal artery, which was preoperatively embolized. Intervention Gross total resection was performed via a translabyrinthine approach. Conclusion The case presented is unique; the first reported AFH at the jugular foramen and the first reported case utilizing preoperative embolization. Preoperative embolization is a relatively safe technique that can improve the surgeon\'s ability to perform a maximally safe resection, which may decrease the need for adjuvant radiation in rare skull base tumors in young patients.
摘要：
目的我们描述第一例颈静脉孔血管瘤样纤维组织细胞瘤（AFH）和术前血管内栓塞的首次治疗。AFH是一种罕见的颅内肿瘤，主要见于儿科患者四肢。随着AFH意识的提高和良好的遗传档案，颅内患病率也随之增加.研究设计我们使用PubMed/Medline文献检索将此病例与以前报告的病例进行比较，使用算法[\"颅内\"和\"血管瘤样纤维组织细胞瘤\"]进行到2020年12月(23份手稿,46例独特病例)。患者一名8岁女性表现为不能茁壮成长和右侧听力损失。检查显示没有右侧可用的听力和大的颈静脉孔肿块。血管造影显示咽升动脉后支的原发性动脉供应，术前栓塞。通过经迷路入路进行了总切除。结论所介绍的病例是独特的；首次报告颈静脉孔AFH，首次报告术前栓塞病例。术前栓塞是一种相对安全的技术，可以提高外科医生进行最大安全切除的能力，这可能会减少年轻患者对罕见颅底肿瘤的辅助放疗的需要。
