PDF(Pubmed)
Abstract：
Biliary atresia (BA) and choledochal cysts are diseases of the intrahepatic and extrahepatic biliary tree. While their exact etiopathogeneses are not known, they should be treated promptly due to the potential for irreversible parenchymal liver disease. A diagnosis of BA may be easy or complicated, but should not be delayed. BA is always treated surgically, and performing the surgery before the age of 2 mo greatly increases its effectiveness and extends the time until the need for liver transplantation arises. While the more common types of choledochal cysts require surgical treatment, some can be treated with endoscopic retrograde cholangiopancreatography. Choledochal cysts may cause recurrent cholangitis and the potential for malignancy should not be ignored.
摘要：
胆道闭锁（BA）和胆总管囊肿是肝内和肝外胆道树的疾病。虽然他们的确切病因尚不清楚，由于可能发生不可逆的肝实质疾病,应及时治疗.BA的诊断可能容易或复杂，但不应该拖延。BA总是手术治疗，在2个月之前进行手术大大提高了其有效性，并延长了需要肝移植的时间。虽然更常见类型的胆总管囊肿需要手术治疗，有些可以用内镜逆行胰胆管造影术治疗。胆总管囊肿可引起复发性胆管炎，恶性肿瘤的可能性不容忽视。
