Abstract：
BACKGROUND: Congenital myasthenia syndrome is a heterogeneous disease with impaired neuromuscular transmission.
METHODS: This report describes a 13-year-old child with congenital myasthenia syndrome who underwent surgery for scoliosis under general anesthesia. We used a small dose of rocuronium, neuromuscular transmission monitoring, and non-invasive positive pressure ventilation for postoperative respiratory management. There were no respiratory complications during the perioperative period.
CONCLUSIONS: As there are only a few reports on the anesthetic management of patients with congenital myasthenia syndrome, we applied the principles of managing autoimmune myasthenia gravis. The postoperative management described herein can prevent respiratory complications in patients with congenital myasthenia syndrome.
METHODS: This report describes a 13-year-old child with congenital myasthenia syndrome who underwent surgery for scoliosis under general anesthesia. We used a small dose of rocuronium, neuromuscular transmission monitoring, and non-invasive positive pressure ventilation for postoperative respiratory management. There were no respiratory complications during the perioperative period.
CONCLUSIONS: As there are only a few reports on the anesthetic management of patients with congenital myasthenia syndrome, we applied the principles of managing autoimmune myasthenia gravis. The postoperative management described herein can prevent respiratory complications in patients with congenital myasthenia syndrome.
摘要：
背景：先天性肌无力综合征是一种神经肌肉传递受损的异质性疾病。
方法：本报告描述了一名患有先天性肌无力综合征的13岁儿童，他在全身麻醉下接受了脊柱侧凸手术。我们用了小剂量的罗库溴铵,神经肌肉传递监测，无创正压通气用于术后呼吸管理。围手术期无呼吸道并发症。
结论：由于关于先天性肌无力综合征患者的麻醉管理的报道很少，我们应用了自身免疫性重症肌无力治疗的原则.本文所述的术后管理可以预防患有先天性肌无力综合征的患者的呼吸系统并发症。
方法：本报告描述了一名患有先天性肌无力综合征的13岁儿童，他在全身麻醉下接受了脊柱侧凸手术。我们用了小剂量的罗库溴铵,神经肌肉传递监测，无创正压通气用于术后呼吸管理。围手术期无呼吸道并发症。
结论：由于关于先天性肌无力综合征患者的麻醉管理的报道很少，我们应用了自身免疫性重症肌无力治疗的原则.本文所述的术后管理可以预防患有先天性肌无力综合征的患者的呼吸系统并发症。
