关键词: Biliary hamartoma Von Meyenburg complexes adenocarcinoma case report ductal plate malformation Biliary hamartoma Von Meyenburg complexes adenocarcinoma case report ductal plate malformation Biliary hamartoma Von Meyenburg complexes adenocarcinoma case report ductal plate malformation

Mesh : Adenocarcinoma Aged, 80 and over Bile Duct Diseases / diagnosis pathology Female Gastrointestinal Neoplasms Hamartoma / pathology Humans Liver Diseases / diagnosis Male Middle Aged Adenocarcinoma Aged, 80 and over Bile Duct Diseases / diagnosis pathology Female Gastrointestinal Neoplasms Hamartoma / pathology Humans Liver Diseases / diagnosis Male Middle Aged

来  源:   DOI:10.11604/pamj.2022.42.57.29748   PDF(Pubmed)

Abstract:
Biliary hamartoma, also known as biliary micro hamartoma or Von Meyenburg complex, is a rare benign liver lesion, thought to be a ductal plate malformation rather than a true neoplasm. It is often seen incidentally on imagery or surgery as multiple small subcapsular nodules, scattered throughout the liver, making it likely to be mistaken for metastatic nodules. The histological presentation can also be deceptive, leading to the misdiagnosis of an adenocarcinoma of hepato-biliary differentiation or a metastasis. We hereby present two cases of biliary hamartoma, found incidentally on imagery and surgery, the first one in a 94-year-old woman, and the second in a 48-year-old man, which was initially misdiagnosed as an adenocarcinoma, along with a discussion of key clinical and pathological findings to help avoid this diagnostic pitfall.
摘要:
胆道错构瘤,也被称为胆道微错构瘤或冯·梅恩堡复合体,是一种罕见的良性肝脏病变,被认为是导管板畸形而不是真正的肿瘤。通常在影像或手术中偶然发现为多个小囊下结节,散布在整个肝脏,很可能被误认为是转移性结节.组织学表现也可能是欺骗性的,导致肝胆分化或转移腺癌的误诊。我们在此介绍两例胆道错构瘤,偶然发现在图像和手术上,第一个94岁的老妇人,第二个是48岁的男人,最初被误诊为腺癌,以及对关键临床和病理结果的讨论,以帮助避免这种诊断缺陷。
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