PDF(Pubmed)
Abstract：
BACKGROUND: Plexiform neurofibroma is a benign tumor of the peripheral nerves. It is an unusual variant of neurofibroma originating from all parts of the nerve. Plexiform neurofibroma is primarily pathognomonic and exhibits an unusual variant from neurofibromatosis type 1 (NF1). The possibility of malignancy and recurrence are the main reasons for long-term, close follow-up.
METHODS: The authors report a case of a 14-year-old girl with a recurrent plexiform neurofibroma derived from the peripheral nerves, which also presented with a typical sign of NF1 disease. The aim of the tumor resection is symptomatic relief.
CONCLUSIONS: Accomplishing a good outcome can be related to good perioperative planning and a precise operative procedure. The result of anatomical pathology determines the prognosis of the patient. Clinical examination and radiological studies are needed to evaluate the recurrence of complications after surgical procedures.
METHODS: The authors report a case of a 14-year-old girl with a recurrent plexiform neurofibroma derived from the peripheral nerves, which also presented with a typical sign of NF1 disease. The aim of the tumor resection is symptomatic relief.
CONCLUSIONS: Accomplishing a good outcome can be related to good perioperative planning and a precise operative procedure. The result of anatomical pathology determines the prognosis of the patient. Clinical examination and radiological studies are needed to evaluate the recurrence of complications after surgical procedures.
摘要：
背景：丛状神经纤维瘤是一种周围神经良性肿瘤。它是源自神经所有部分的神经纤维瘤的不寻常变体。丛状神经纤维瘤主要是病理性的，表现出1型神经纤维瘤病（NF1）的异常变异。恶性肿瘤和复发的可能性是长期的主要原因,密切跟进。
方法：作者报告了一例14岁女孩，患有源自周围神经的复发性丛状神经纤维瘤，这也是NF1疾病的典型征兆。肿瘤切除的目的是缓解症状。
结论：取得良好的结果可能与良好的围手术期计划和精确的手术程序有关。解剖病理学的结果决定了患者的预后。需要进行临床检查和放射学研究以评估外科手术后并发症的复发。
方法：作者报告了一例14岁女孩，患有源自周围神经的复发性丛状神经纤维瘤，这也是NF1疾病的典型征兆。肿瘤切除的目的是缓解症状。
结论：取得良好的结果可能与良好的围手术期计划和精确的手术程序有关。解剖病理学的结果决定了患者的预后。需要进行临床检查和放射学研究以评估外科手术后并发症的复发。
