Abstract：
Myotonic dystrophy type 1 or Steinert\'s disease is an autosomal dominant multisystem disease which is characterized by consistent contracture of muscle following stimulation (myotonia). Hypothermia, shivering, mechanical or electric stimulation during surgery can precipitate episodes of myotonia which may complicate the course of anaesthesia. The present case report focuses on successful strategies for providing general anaesthesia for laparoscopic cholecystectomy in a patient affected by this genetic disorder, at a hospital which does not have the facility for postoperative ventilation.
摘要：
强直性肌营养不良1型或Steinert病是一种常染色体显性遗传多系统疾病，其特征是刺激后肌肉一致挛缩（肌强直）。体温过低,颤抖,手术过程中的机械或电刺激会导致肌强直发作，这可能会使麻醉过程复杂化。本病例报告着重于成功的策略，为患有这种遗传性疾病的患者提供腹腔镜胆囊切除术的全身麻醉。在没有术后通气设施的医院。
