Abstract：
Arrhythmogenic right ventricular dysplasia (ARVD) is a progressive degeneration and replacement of the right ventricular (RV) myocardial tissue by fat and fibrosis and produce clinical condition. Desmosome gene mutations are only the causative state for ARVD hereditary disorder. The arrhythmogenic right ventricular cardiomyopathy incidence is about 1/1000-5000. Mostly young people and athletes are bearing the clinical presentations include presyncope, syncope, ventricular tachycardias or ventricular fibrillation leading to cardiac arrest. We report about the first case of Cardiac magnetic resonance (CMR) imaging to diagnose a case Arrhythmogenic right ventricular dysplasia (ARVD) of a 34-year-old male from Savar, Dhaka, Bangladesh who was referred to cardiac emergency for the evaluation recurrent dizzy spells.
摘要：
致心律失常性右心室发育不良(ARVD)是由脂肪和纤维化构成的右心室(RV)心肌组织的进行性变性和替换而产生的临床状况。桥粒基因突变只是ARVD遗传性疾病的致病状态。致心律失常性右心室心肌病的发生率约为1/1000-5000。大多数年轻人和运动员的临床表现包括晕厥前，晕厥,室性心动过速或室颤导致心脏骤停。我们报告了首例心脏磁共振（CMR）成像诊断一例Savar一名34岁男性的心律失常性右心室发育不良（ARVD），达卡,孟加拉国因评估复发性头晕而被称为心脏急诊。
