PDF(Pubmed)
Abstract：
Fibrous dysplasia has various ways of presentation including syndromic associations and secondary changes within the lesion. We present a case of a 21-year-old female with craniofacial fibrous dysplasia, presenting with proptosis and intermittent blurring of vision due to focal fibrous dysplasia involving the frontal bone with secondary aneurysmal bone formation that was provisionally diagnosed on imaging and confirmed on histopathology. This case demonstrates the typical imaging findings of fibrous dysplasia with seldom encountered secondary aneurysmal bone cyst formation and also discusses about the pathology and management of the craniofacial fibrous dysplasia.
摘要：
纤维发育不良有多种表现方式，包括综合征性关联和病变内的继发性变化。我们介绍一例21岁女性颅面纤维发育不良，由于涉及额骨的局灶性纤维发育不良伴继发性动脉瘤性骨形成，出现眼球突出和间歇性视力模糊，影像学暂时诊断并在组织病理学上得到证实。此病例显示了纤维发育不良的典型影像学表现，很少遇到继发性动脉瘤性骨囊肿形成，并讨论了颅面纤维发育不良的病理和处理方法。
